2019 Updated Consensus Statement on the Diagnosis and Treatment of Pediatric Pulmonary Hypertension

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Published 21 June 2019

Georg Hansmann, MD, PhD; Martin Koestenberger, MD; Tero-Pekka Alastalo, MD, PhD; Christian Apitz, MD; Eric D. Austin, MD, MSc; Damien Bonnet, MD, PhD; Werner Budts, MD, PhD; Michele D'Alto, MD, PhD; Michael A. Gatzoulis, MD, PhD; Babar S. Hasan, MD; Rainer Kozlik-Feldmann, MD; R. Krishna Kumar, MD; Astrid E. Lammers, MD, MD(Res); Heiner Latus, MD; Ina Michel-Behnke, MD, PhD; Oliver Miera, MD; Nicholas W. Morrell, MD; Guido Pieles, MD, DPhil; Daniel Quandt, MD; Hannes Sallmon, MD; Dietmar Schranz, MD; Karin Tran-Lundmark, MD, PhD; Robert M.R. Tulloh, DM FRCPCH; Gregor Warnecke, MD; Håkan Wåhlander, MD, PhD; Sven C. Weber, MD; Peter Zartner, MD

J Heart Lung Transplant. 2019 Sep;38(9):879-901

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European Pediatric Pulmonary Vascular Disease Network (EPPVDN)

The 2015 European Society of Cardiology (ESC) and European Respiratory Society guidelines on the diagnosis and treatment of PH includes comprehensive recommendations on the diagnosis and treatment of PH but mainly focuses on clinical care in adults. In 2016, the EPPVDN published a multipaper consensus statement that contains practical recommendations for health care providers treating children and adolescents with different forms of PH. This 2019 update to the 2016 consensus recommendations was created to deliver an updated, comprehensive, practical guidelines for healthcare providers addressing the specifics of PH and PVD in children and young adults.

Topics include diagnosis/monitoring, genetics/biomarkers, cardiac catheterization, echocardiography, cardiac magnetic resonance/chest computed tomography, associated forms of PH, intensive care unit/lung transplantation, and treatment of pediatric PH. For the first time, a set of specific recommendations on the management of PH in middle- and low-income regions was developed. Taken together, these executive, up-to-date guidelines provide a specific, comprehensive, detailed but practical framework for the optimal clinical care of children and young adults with PH.

This consensus statement was endorsed by ISHLT in 2019.

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